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Microscopic polyangiitis presenting as idiopathic pulmonary fibrosis

The most detectable form of pulmonary fibrosis in MPA (microscopic polyangiitis) is UIP (usual interstitial pneumonia), occurring in 48 % of MPA patients with pulmonary fibrosis. In some cases, ILD (interstitial lung disease) is the initial clinical manifestation of MPA (22 % of cases). Here, we des...

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Autore principale: Brittany Duchene
Natura: Artigo
Lingua:Inglês
Pubblicazione: Elsevier 2024-01-01
Serie:Respiratory Medicine Case Reports
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Accesso online:http://www.sciencedirect.com/science/article/pii/S221300712400145X
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