A very rare cause of pre‐capillary pulmonary hypertension: The PAMI syndrome

Abstract We report the first known case of PAMI syndrome associated with pulmonary arterial hypertension (PAH) with a positive response to cyclophosphamide and pulmonary vasodilators. The patient's history began at 7 months with severe pancytopenia and fever. As time progressed, migrating arthritis,...

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Bibliografske podrobnosti

Principais autores:	Manuela Iseppi, Giulio Savonitto, Alberto Tommasini, Alessia Pin, Gianfranco Sinagra, Davide Stolfo
Format:	Artigo
Jezik:	Inglês
Izdano:	Wiley 2023-10-01
Serija:	Pulmonary Circulation
Teme:	inflammatory PH interferonopathies PSTPIP1 gene pulmonary arterial hypertension (PAH) pulmonary circulation
Online dostop:	https://doi.org/10.1002/pul2.12300
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