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Impact on Body Composition After Two Years of Elexacaftor–Tezacaftor–Ivacaftor Therapy in Children with Cystic Fibrosis

<b>Background:</b> Triple therapy with cystic fibrosis transmembrane conductance regulator (CFTR) modulators in patients with cystic fibrosis (CF) has led to a shift in the nutritional management of the disease. Correct assessment of nutritional status is crucial due to its significant impact in pul...

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Bibliografiske detaljer
Principais autores: María Álvarez Merino, Concepción Marina López Cárdenes, Saray Mesonero Cavia, Encarnación Torcuato Rubio, Alejandro Rodríguez-Martínez, Saioa Vicente Santamaría, Clara Viñas Torne, Marina Álvarez Beltrán, Celia Gascón Galindo, María Garriga García, Ana Muñoz Alonso, Mercedes Murray Hurtado, Sara Sierra San Nicolás, Pilar Ortiz-Pérez, José Ramón Gutiérrez Martínez, Marta Suárez González, David González Jiménez, Juan José Díaz Martín
Format: Artigo
Sprog:Inglês
Udgivet: MDPI AG 2025-11-01
Serier:Children
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Online adgang:https://www.mdpi.com/2227-9067/12/12/1598
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