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Congenital tracheobronchomegaly (Mounier-Kuhn syndrome) in a 70-year-old nonsmoking male: A rare presentation in a low-resource setting

Background: Mounier-Kuhn Syndrome (MKS), or congenital tracheobronchomegaly, is a rare disorder characterized by dilation of the trachea and main bronchi due to the atrophy of elastic and smooth muscle fibers. Though often associated with recurrent infections, it may be underdiagnosed, particularly...

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Autores principales: Yousif Aboaziza, Eiman Aboaziza, Rabha E. Almahdi, Abdelrahman Aboaziza, Samira H. Belkheir
Formato: Artigo
Lenguaje:Inglês
Publicado: Elsevier 2025-01-01
Colección:Respiratory Medicine Case Reports
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Acceso en línea:http://www.sciencedirect.com/science/article/pii/S2213007125001364
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