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Study of very long chain acyl-CoA dehydrogenase (VLCAD) with cardiomyopathy using a deuterated substrate

Introduction: Deficiency of VLCAD is present in the early months of life, with hypertrophic or dilated cardiomyopathy and arrhythmias which may be lethal. Objective: To analize the production of metabolites in fibroblasts from patientes with VLCAD deficiency and cardiomyopathy incubated with deu...

Бүрэн тодорхойлолт

-д хадгалсан:
Номзүйн дэлгэрэнгүй
Үндсэн зохиолч: Osorio, José Henry
Формат: Artigo
Хэл сонгох:Espanhol
Хэвлэсэн: Universidad de Antioquia 2014-10-01
Цуврал:Iatreia
Нөхцлүүд:
Онлайн хандалт:http://aprendeenlinea.udea.edu.co/revistas/index.php/iatreia/article/view/15098/17394
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