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Management of pulmonary arterial hypertension in systemic sclerosis: from classical treatments to new horizons

Pulmonary arterial hypertension (PAH) is a severe disease characterised by a progressive thickening and obliteration of pulmonary vessels, resulting in increased vascular resistance, elevated pulmonary artery pressures, and right heart failure. Among the various conditions associated with PAH, syste...

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Hlavní autoři: Annalisa Villa, Sébastien Sanges, Vincent Sobanski, Nicolas Lamblin, Edoardo Rosato, Laurent Godinas, Eric Hachulla, Marion Delcroix, David Montani, David Launay
Médium: Artigo
Jazyk:Inglês
Vydáno: European Respiratory Society 2026-02-01
Edice:European Respiratory Review
On-line přístup:https://doi.org/10.1183/16000617.0137-2025
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