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Quantification of sulfatides and lysosulfatides in tissues and body fluids by liquid chromatography-tandem mass spectrometry[S]

Sulfatides are found in brain as components of myelin, oligodendrocytes, and neurons but are also present in various visceral tissues. Metachromatic leukodystrophy (MLD) is an inherited lysosomal storage disorder caused by a deficiency of arylsulfatase A, leading to severe white matter disease due t...

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Principais autores: Mina Mirzaian, Gertjan Kramer, Ben J.H.M. Poorthuis
Formato: Artigo
Idioma:Inglês
Publicado: Elsevier 2015-04-01
Series:Journal of Lipid Research
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Acceso en liña:http://www.sciencedirect.com/science/article/pii/S0022227520355747
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