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Audiometric evaluation in individuals with mucopolysaccharidosis

OBJECTIVES: To characterize the audiometric evaluation and acoustic immittance measures in different types of mucopolysaccharidosis. METHOD: Fifty-three mucopolysaccharidosis patients were evaluated. The classification consisted of type I (Hurler syndrome, Hurler-Scheie and Scheie syndrome), type I...

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Autori principali: Marcela Rosana Maia da Silveira, Ana Karina Lima Buriti, Ana Maria Martins, Daniela Gil, Marisa Frasson de Azevedo
Natura: Artigo
Lingua:Inglês
Pubblicazione: Elsevier España 2018-12-01
Serie:Clinics
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Accesso online:http://www.scielo.br/scielo.php?script=sci_arttext&pid=S1807-59322018000100297&lng=en&tlng=en
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