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Early Tonsillectomy for Dual Remission of Periodic Fever, Aphthous Stomatitis, Pharyngitis, and Adenitis Syndrome and Immunoglobulin A Nephropathy: A Case Report

Despite sharing tonsillar immune dysregulation as a common pathogenic mechanism, concurrent presentation of periodic fever, aphthous stomatitis, pharyngitis, and adenitis (PFAPA) syndrome with immunoglobulin A (IgA) nephropathy (IgAN) remains exceptionally rare, with only 1 previous case reported in...

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Hlavní autoři: Daishi Hirano, Kensuke Joh, Shiko Honma, Ryoko Sakaguchi, Aya Saito, Yuna Hiwatari, Shiho Yoshizawa, Yosuke Shoji, Haruhide Sakaguchi, Chisato Umeda, Saori Miwa, Akira Ito
Médium: Artigo
Jazyk:Inglês
Vydáno: Elsevier 2026-07-01
Edice:Kidney Medicine
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On-line přístup:http://www.sciencedirect.com/science/article/pii/S259005952600138X
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