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Bronchial obstruction in osteogenesis imperfecta can be detected by forced oscillation technique

IntroductionRespiratory insufficiency is a leading cause of death in individuals with osteogenesis imperfecta (OI). However, evaluating pulmonary function in OI presents challenges. Commonly used pulmonary function tests such as spirometry and body plethysmography are sometimes difficult to perform...

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Autors principals: Silvia Storoni, Sara J. E. Verdonk, Dimitra Micha, Patrick M. C. Jak, Marianna Bugiani, Elisabeth M. W. Eekhoff, Joost G. van den Aardweg
Format: Artigo
Idioma:Inglês
Publicat: Frontiers Media S.A. 2023-12-01
Col·lecció:Frontiers in Medicine
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Accés en línia:https://www.frontiersin.org/articles/10.3389/fmed.2023.1301873/full
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