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Idiopathic pleuroparenchymal fibroelastosis in a patient with pectus excavatum: an overlooked association

Pleuroparenchymal fibroelastosis (PPFE) is a rare, progressive interstitial lung disease characterised by prominent upper lobe fibrosis and elastotic changes. Its aetiology remains unclear, with most cases classified as idiopathic. While pectus excavatum has been noted in some PPFE cases, its poten...

Бүрэн тодорхойлолт

-д хадгалсан:
Номзүйн дэлгэрэнгүй
Үндсэн зохиолчид: K. Maduranga, A. P. D. Manodhya, S. Palihawadene, E. Perara
Формат: Artigo
Хэл сонгох:Inglês
Хэвлэсэн: Sri Lanka College of Internal Medicine 2025-08-01
Цуврал:Asian Journal of Internal Medicine
Нөхцлүүд:
Онлайн хандалт:https://account.ajim.sljol.info/index.php/sljo-j-ajim/article/view/279
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