Paroxysmal Nocturnal Hemoglobinuria (PNH): A Comprehensive Review
Paroxysmal nocturnal haemoglobinuria (PNH) is a rare, acquired clonal hemopoietic stem cell disorder characterized by complement mediated chronic intravascular haemolysis, bone marrow failure and life-threatening thrombosis. PNH results from a somatic mutation in the PIG-A gene on the X chromosome...
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| Formatua: | Artigo |
| Hizkuntza: | Inglês |
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Haematology Society of Bangladesh
2026-01-01
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| Saila: | Haematology Journal of Bangladesh |
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| Sarrera elektronikoa: | https://journal.hematologybd.org/index.php/haematoljbd/article/view/150 |
| Etiketak: |
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