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Paroxysmal Nocturnal Hemoglobinuria (PNH): A Comprehensive Review

Paroxysmal nocturnal haemoglobinuria (PNH) is a rare, acquired clonal hemopoietic stem cell disorder characterized by complement mediated chronic intravascular haemolysis, bone marrow failure and life-threatening thrombosis. PNH results from a somatic mutation in the PIG-A gene on the X chromosome...

Deskribapen osoa

Gorde:
Xehetasun bibliografikoak
Egile nagusia: Muhammad Kamruzzaman
Formatua: Artigo
Hizkuntza:Inglês
Argitaratua: Haematology Society of Bangladesh 2026-01-01
Saila:Haematology Journal of Bangladesh
Gaiak:
Sarrera elektronikoa:https://journal.hematologybd.org/index.php/haematoljbd/article/view/150
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