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Ethnicity affects relapse-free survival in immune-mediated thrombotic thrombocytopenic purpura

Immune-mediated thrombotic thrombocytopenic purpura (iTTP) is caused by a severe, antibody-mediated deficiency of ADAMTS13 (A Disintegrin And Metalloproteinase with ThromboSpondin-1 motifs, 13th member) activity. The B-cell depleting agent rituximab is effective in restoring ADAMTS13 activity and t...

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Autors principals: Júlia Weisinger, Florian Blanchard, Benoit Suzon, Christophe Deligny, Jehane Fadlallah, François Provôt, Pascale Poullin, Manon Marie, David Ribes, Gabriel Choukroun, Yahsou Delmas, Elie Azoulay, Ygal Benhamou, Maximilien Grall, Jean-Michel Halimi, Moglie Le Quintrec, Aude Servais, Thomas Papo, Camille Lepart, Claire Cartery, Valérie Chatelet, Jean-Francois Augusto, Simon Ville, Pierre Perez, Loïc Lièvre, Mathieu Legendre, Anne Rumpler, Alexandre Hertig, Virginie Rieu, Arnaud Jaccard, Patricia Zunic, Laurent Gilardin, Nihal Martis, Sara Rovira Puig, Rutuja Gupte, Maria del Mar Tolos Garcia, Margot Dierickx, Daniela Greco, Timon Albrecht, Andreea-Adela Icleanu, Raïda Bouzid, Bérangère Joly, Agnès Veyradier, Adrien Picod, Paul Coppo
Format: Artigo
Idioma:Inglês
Publicat: Ferrata Storti Foundation 2026-01-01
Col·lecció:Haematologica
Accés en línia:https://haematologica.org/article/view/13082
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