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Association between Cowden syndrome and Lhermitte-Duclos disease: A case report of an uncommon Genetic Hamartomatous Disorder

The dysplastic gangliocytoma of the cerebellum, also known as Lhermitte-Duclos disease, is an uncommon hamartomatous lesion in the posterior fossa with some distinctive neuroradiological characteristics. It can happen in combination with Cowden syndrome or sporadically. Cowden disease, or multiple h...

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-д хадгалсан:
Номзүйн дэлгэрэнгүй
Үндсэн зохиолчид: Hanane El Aggari, MD, Siham Nasri, MD, Ahsayen Fatima Zohra, MD, Narjisse Aichouni, MD, Imane Kamaoui, MD, Imane Skiker, MD
Формат: Artigo
Хэл сонгох:Inglês
Хэвлэсэн: Elsevier 2023-08-01
Цуврал:Radiology Case Reports
Нөхцлүүд:
Онлайн хандалт:http://www.sciencedirect.com/science/article/pii/S1930043323003023
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