Intractable metabolic acidosis in a child with propionic acidemia undergoing liver transplantation -a case report-
Propionic acidemia (PA) is a rare autosomal recessive disorder of metabolism caused by deficient activity of the mitochondrial enzyme propionyl-CoA carboxylase. The clinical manifestations are metabolic acidosis, poor feeding, lethargy, vomiting, osteoporosis, neurological dysfunction, pancytopenia,...
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| Principais autores: | , , , , |
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| Formato: | Artigo |
| Idioma: | Inglês |
| Publicado em: |
Korean Society of Anesthesiologists
2013-09-01
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| coleção: | Korean Journal of Anesthesiology |
| Assuntos: | |
| Acesso em linha: | http://ekja.org/upload/pdf/kjae-65-257.pdf |
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