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Macrophage Activation-Like Syndrome: A Distinct Entity Leading to Early Death in Sepsis

Hemophagocytic lymphohistocytosis (HLH) is characterized by fulminant cytokine storm leading to multiple organ dysfunction and high mortality. HLH is classified into familial (fHLH) and into secondary (sHLH). fHLH is rare and it is due to mutations of genes encoding for perforin or excretory granule...

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Principais autores: Eleni Karakike, Evangelos J. Giamarellos-Bourboulis
Formato: Artigo
Idioma:Inglês
Publicado: Frontiers Media S.A. 2019-01-01
Series:Frontiers in Immunology
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Acceso en liña:https://www.frontiersin.org/article/10.3389/fimmu.2019.00055/full
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