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Clinical, radiological and histopathological features of patients with familial pulmonary fibrosis

Abstract Background In familial pulmonary fibrosis (FPF) at least two biological relatives are affected. Patients with FPF have diverse clinical features. Research question We aimed to characterize demographic and clinical features, re-evaluate high-resolution computed tomography (HRCT) scans and hi...

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Autores principales: Hanna Jaula, Lauri Mattila, Elisa Lappi-Blanco, Johanna Salonen, Hannu Vähänikkilä, Lauri Ahvenjärvi, Jukka S. Moilanen, Outi Kuismin, Terttu Harju, Riitta Kaarteenaho
Formato: Artigo
Lenguaje:Inglês
Publicado: BMC 2024-06-01
Colección:Respiratory Research
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Acceso en línea:https://doi.org/10.1186/s12931-024-02864-5
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