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Niemann - Pick disease associated with hemophagocytic syndrome

Hemophagocytic lymphohistiocytosis (HLH) is a disease characterized by phagocytosis of blood cells by macrophages within the lymphoreticular tissue. It can develop secondary to some diseases or be familial as a result of genetic mutations. Niemann-Pick disease (NPD) is a very rare lipid storage dise...

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Autores principales: Serap Karaman, Nafiye Urgancı, Günsel Kutluk, Feyzullah Çetinkaya
Formato: Artigo
Lenguaje:Inglês
Publicado: Turkish Society of Hematology 2010-12-01
Colección:Turkish Journal of Hematology
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Acceso en línea:https://jag.journalagent.com/z4/download_fulltext.asp?pdir=tjh&un=TJH-99815
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