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Mechanisms of CFTR folding at the endoplasmic reticulum

In the past decade much has been learned about how CFTR folds and misfolds as the etiologic cause of cystic fibrosis (CF). CFTR folding is complex and hierarchical, takes place in multiple cellular compartments and physical environments, and involves several large networks of folding machineries. I...

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Autori principali: Soo Jung Kim, William R Skach
Natura: Artigo
Lingua:Inglês
Pubblicazione: Frontiers Media S.A. 2012-12-01
Serie:Frontiers in Pharmacology
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Accesso online:http://journal.frontiersin.org/Journal/10.3389/fphar.2012.00201/full
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