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Towards a histological diagnosis of childhood small vessel CNS vasculitis

Abstract Background Primary small vessel CNS vasculitis (sv-cPACNS) is a challenging inflammatory brain disease in children. Brain biopsy is mandatory to confirm the diagnosis. This study aims to develop and validate a histological scoring tool for diagnosing small vessel CNS vasculitis. Methods A s...

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Autores principales: Maryam Nabavi Nouri, Anastasia Dropol, Pascal N. Tyrrell, Sheila Sheikh, Marinka Twilt, Jean Michaud, Benjamin Ellezam, Harvey B. Sarnat, Christopher Dunham, Peter W. Schutz, Julia Keith, David G. Munoz, Harry V. Vinters, Cynthia Hawkins, Susanne M. Benseler
Formato: Artigo
Lenguaje:Inglês
Publicado: BMC 2024-12-01
Colección:Pediatric Rheumatology Online Journal
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Acceso en línea:https://doi.org/10.1186/s12969-024-01053-4
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