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Early risk prediction in idiopathic versus connective tissue disease-associated pulmonary arterial hypertension: call for a refined assessment

Despite systematic screening and improved treatment strategies, the prognosis remains worse in patients with connective tissue disease-associated pulmonary arterial hypertension (CTD-PAH) compared to patients with idiopathic/hereditary pulmonary arterial hypertension (IPAH). We aimed to investigate...

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Detalles Bibliográficos
Principais autores: Clara Hjalmarsson, Barbro Kjellström, Kjell Jansson, Magnus Nisell, David Kylhammar, Mohammad Kavianipour, Göran Rådegran, Stefan Söderberg, Gerhard Wikström, Dirk M. Wuttge, Roger Hesselstrand
Formato: Artigo
Idioma:Inglês
Publicado: European Respiratory Society 2021-08-01
Series:ERJ Open Research
Acceso en liña:http://openres.ersjournals.com/content/7/3/00854-2020.full
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