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Why, when and how to investigate primary ciliary dyskinesia in adult patients with bronchiectasis

Abstract Bronchiectasis represents the final pathway of several infectious, genetic, immunologic or allergic disorders. Accurate and prompt identification of the underlying cause is a key recommendation of several international guidelines, in order to tailor treatment appropriately. Primary ciliary...

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Autors principals: Martina Contarini, Amelia Shoemark, Jessica Rademacher, Simon Finch, Andrea Gramegna, Michele Gaffuri, Luca Roncoroni, Manuela Seia, Felix C. Ringshausen, Tobias Welte, Francesco Blasi, Stefano Aliberti, James D. Chalmers
Format: Artigo
Idioma:Inglês
Publicat: Mattioli 1885 2018-08-01
Col·lecció:Multidisciplinary Respiratory Medicine
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Accés en línia:http://link.springer.com/article/10.1186/s40248-018-0143-6
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