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Improvement of Cystic Fibrosis-Associated Liver Disease in Adults on Long-Term Cystic Fibrosis Transmembrane Conductance Regulator (CFTR) Modulators

Cystic fibrosis (CF) transmembrane conductance regulator (CFTR) modulators have been reported to improve lung function and reduce CF exacerbations. We aimed to investigate the efficacy of CFTR-modulators in CF-associated liver disease (CFLD) during long-term treatment. Longitudinal data were collect...

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-д хадгалсан:
Номзүйн дэлгэрэнгүй
Үндсэн зохиолчид: Sofia Manioudaki, Larisa Vasilieva, Eleni Geladari, Iliana Mani, Zoe Athanassa, Ioannis Elefsiniotis, Emilia Hadziyannis, Vasilios Sevastianos, Aikaterini Oikonomou, Andreas Theophilou, Filia Diamantea, Alexandra Alexopoulou
Формат: Artigo
Хэл сонгох:Inglês
Хэвлэсэн: MDPI AG 2025-11-01
Цуврал:Life
Нөхцлүүд:
Онлайн хандалт:https://www.mdpi.com/2075-1729/15/12/1794
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