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Assessing Gut Microbiota in an Infant with Congenital Propionic Acidemia before and after Probiotic Supplementation

Propionic Acidemia (PA) is a rare inherited metabolic disorder caused by the enzymatic block of propionyl-CoA carboxylase with the consequent accumulation of propionic acid, which is toxic for the brain and cardiac cells. Since a considerable amount of propionate is produced by intestinal bacteria,...

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Autors principals: Andrea Bordugo, Elisa Salvetti, Giulia Rodella, Michele Piazza, Alice Dianin, Angela Amoruso, Giorgio Piacentini, Marco Pane, Sandra Torriani, Nicola Vitulo, Giovanna E. Felis
Format: Artigo
Idioma:Inglês
Publicat: MDPI AG 2021-12-01
Col·lecció:Microorganisms
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Accés en línia:https://www.mdpi.com/2076-2607/9/12/2599
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