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PCSK6 and clinical outcomes in the Pulmonary Fibrosis Foundation Patient Registry

Abstract Background Higher plasma proprotein convertase subtilisin/kexin type 6 (PCSK6) concentration has been associated with increased all-cause mortality in idiopathic pulmonary fibrosis (IPF). Its role across the broader spectrum of fibrotic interstitial lung disease (ILDs) remains unclear. We e...

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Autors principals: Kristin Berger, Sam Konkol, Shwu-Fan Ma, William Whalen, Will Simmons, Chitra Joseph, Imre Noth, Yong Huang, Justin Oldham, Christopher A. Moskaluk, David Lynch, Stephen Humphries, John S. Kim, Anna J. Podolanczuk
Format: Artigo
Idioma:Inglês
Publicat: BMC 2026-04-01
Col·lecció:Respiratory Research
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Accés en línia:https://doi.org/10.1186/s12931-026-03642-1
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