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PKD1 deficiency induces Bronchiectasis in a porcine ADPKD model

Abstract Background Autosomal dominant polycystic kidney disease (ADPKD) is a prevalent genetic disorder, mainly characterized by the development of renal cysts, as well as various extrarenal manifestations. Previous studies have shown that ADPKD is related to bronchiectasis, while its pathogenic me...

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Wedi'i Gadw mewn:
Manylion Llyfryddiaeth
Prif Awduron: Runming Wang, Wenya Li, Haiting Dai, Mingli Zhu, Lingyu Li, Guohui Si, Yilina Bai, Hanyu Wu, Xiaoxiang Hu, Yiming Xing
Fformat: Artigo
Iaith:Inglês
Cyhoeddwyd: BMC 2022-10-01
Cyfres:Respiratory Research
Pynciau:
Mynediad Ar-lein:https://doi.org/10.1186/s12931-022-02214-3
Tagiau: Ychwanegu Tag
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