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Clinical Case of X-Linked Lymphoproliferative Syndrome Burdened with Hemophagocytic Lymphohistiocytosis and Crohn's Disease

Background. X-linked lymphoproliferative (XLP) syndrome is hereditary disease with the incidence of 1-3 per 1 million born boys. This clinical case demonstrates a rare picture of XLP type 2 manifestation without prior Epstein-Barr virus.Clinical case description. Boy D., 15 years old, was admitted t...

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Autors principals: Ekaterina S. Matros, Alena I. Karitskaya
Format: Artigo
Idioma:Russo
Publicat: Union of pediatricians of Russia 2023-03-01
Col·lecció:Педиатрическая фармакология
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Accés en línia:https://www.pedpharma.ru/jour/article/view/2269
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