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Hemophilia and hereditary angioedema: parallel therapeutic advances in genetic diseases of serine protease pathways

Hemophilia and hereditary angioedema (HAE) are rare monogenic disorders characterized by the dysregulation of serine protease-based biological pathways, that is, blood coagulation and the kallikrein–kinin system. Although clinical manifestations differ profoundly (bleeding vs angioedema), both disea...

Бүрэн тодорхойлолт

-д хадгалсан:
Номзүйн дэлгэрэнгүй
Үндсэн зохиолчид: Massimo Cugno, Pier Mannuccio Mannucci
Формат: Artigo
Хэл сонгох:Inglês
Хэвлэсэн: Elsevier 2026-03-01
Цуврал:Research and Practice in Thrombosis and Haemostasis
Нөхцлүүд:
Онлайн хандалт:http://www.sciencedirect.com/science/article/pii/S2475037926001147
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