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Lymphangioleiomyomatosis: what do we know and what are we looking for?

Lymphangioleiomyomatosis (LAM) is a rare disease characterised by proliferation of abnormal smooth muscle-like cells (LAM cells) leading to progressive cystic destruction of the lung, lymphatic abnormalities and abdominal tumours. It affects predominantly females and can occur sporadically or in pat...

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Detalles Bibliográficos
Autores principales: O. Torre, S. Harari, J. Moss
Formato: Artigo
Lenguaje:Inglês
Publicado: European Respiratory Society 2011-03-01
Colección:European Respiratory Review
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Acceso en línea:http://err.ersjournals.com/content/20/119/034.full.pdf+html
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