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Bronchiectasis in a patient with Autoimmune Polyendocrinopathy-Candidiasis-Ectodermal Dystrophy: a case report

Abstract Background The rare monogenic syndrome Autoimmune Polyendocrinopathy-Candidiasis-Ectodermal Dystrophy (APECED) leads to multisystemic autoimmunity with possible lung involvement. Autoimmune pneumonitis is a rare manifestation, with bronchiectasis being the most frequent radiologic pattern,...

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Principais autores: Margherita S. Silani, Edoardo Simonetta, Andrea Gramegna, Alessandro De Angelis, Francesco Blasi, Stefano Aliberti
Formato: Artigo
Idioma:Inglês
Publicado: BMC 2024-10-01
Series:BMC Pulmonary Medicine
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Acceso en liña:https://doi.org/10.1186/s12890-024-03149-9
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