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Determinants of adherence to sirolimus among lymphangioleiomyomatosis patients

Abstract Background Lymphangioleiomyomatosis (LAM) is a low-grade malignant neoplasm characterized by multisystem involvement. Patients with LAM require long-term sirolimus therapy to slow disease progression, yet poor adherence to this medication may lead to reduced lung function and disease deteri...

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Autors principals: Li Gao, Yating Peng, Ruoyun Ouyang
Format: Artigo
Idioma:Inglês
Publicat: BMC 2026-02-01
Col·lecció:BMC Pulmonary Medicine
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Accés en línia:https://doi.org/10.1186/s12890-026-04157-7
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