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Diagnosis and management of chronic thromboembolic pulmonary hypertension (CTEPH) in sickle cell disease: A review

Abstract Pulmonary hypertension in sickle cell disease (SCD) is a complex phenomenon resulting from multiple overlapping etiologies, including pulmonary vasoconstriction in the setting of chronic hemolytic anemia, diastolic dysfunction, and chronic thromboembolic disease. The presence of pulmonary h...

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Hlavní autoři: Kadija Hersi, Gautam V. Ramani, Jennie Y. Law, Ahmed S. Sadek, Anjali Vaidya, Mark T. Gladwin, Steven J. Cassady
Médium: Artigo
Jazyk:Inglês
Vydáno: Wiley 2024-04-01
Edice:Pulmonary Circulation
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On-line přístup:https://doi.org/10.1002/pul2.12362
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