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Interleukin-1 Receptor-Associated Kinase 4 Deficiency in a Greek Teenager

Background. Human interleukin- (IL-) 1 receptor-associated kinase 4 (IRAK-4) deficiency is a recently described primary immunodeficiency. It is a rare, autosomal recessive immunodeficiency that impairs toll/IL-1R immunity, except for the toll-like receptor (TLR) 3- and TLR4-interferon alpha (IFNA)/b...

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Autors principals: Panagiota Karananou, Anastasia Alataki, Efimia Papadopoulou-Alataki
Format: Artigo
Idioma:Inglês
Publicat: Wiley 2020-01-01
Col·lecció:Case Reports in Immunology
Accés en línia:http://dx.doi.org/10.1155/2020/8846827
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