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Hypertonic saline in people with cystic fibrosis: review of comparative studies and clinical practice

Abstract Cystic fibrosis (CF) is a multisystem disorder, caused by mutations in the CF transmembrane conductance regulator (CFTR) gene. These cause a reduced secretion of chloride, a marked absorption of sodium and, therefore, of water, through the epithelium, resulting in the formation of thickened...

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Autori principali: Vito Terlizzi, Eleonora Masi, Michela Francalanci, Giovanni Taccetti, Diletta Innocenti
Natura: Artigo
Lingua:Inglês
Pubblicazione: BMC 2021-08-01
Serie:Italian Journal of Pediatrics
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Accesso online:https://doi.org/10.1186/s13052-021-01117-1
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