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Pancreatic Kaposiform Hemangioendothelioma Not Responding to Sirolimus

Abstract Background Kaposiform hemangioendothelioma (KHE) is a vascular tumor frequently associated with Kasabach–Merritt phenomenon (KMP), characterized by severe thrombocytopenia and consumptive coagulopathy. Visceral involvement in KHE is rare. In our recent experience, sirolimus has...

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Bibliografiske detaljer
Principais autores: Paloma Junco Triana, Mariela Dore, Vanesa Cerezo Nuñez, Javier Gomez Jimenez, Miriam Ferrero Miguel, Mercedes González Díaz, Joan Novo Ricardo, Ane Andres, Manuel Lopez Santamaria, Juan Carlos Lopez-Gutierrez
Format: Artigo
Sprog:Inglês
Udgivet: Georg Thieme Verlag KG 2017-01-01
Serier:European Journal of Pediatric Surgery Reports
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Online adgang:http://www.thieme-connect.de/DOI/DOI?10.1055/s-0037-1604358
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