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Retinal Capillary Abnormalities in Sjögren-Larsson Syndrome Maculopathy

Sjögren-Larsson syndrome (SLS) is a neurometabolic disease with a peculiar crystalline maculopathy. It is yet unclear if vascular abnormalities play a role in SLS maculopathy pathogenesis. We used optical coherence tomography angiography (OCT-A) to search for vessel abnormalities in SLS maculopathy....

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Principais autores: Pippa Staps, Anita de Breuk, Johannes R.M. Cruysberg, Michèl Willemsen, Thomas Theelen
Formato: Artigo
Idioma:Inglês
Publicado: Karger Publishers 2022-05-01
Series:Case Reports in Ophthalmology
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Acceso en liña:https://www.karger.com/Article/FullText/524591
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