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Cochlear implant surgery with perimodiolar array insertion in patients with osteogenesis imperfecta: case report and literature review

Osteogenesis imperfecta (OI) is a heterogeneous genetic disease of the connective tissues characterized by a deficit in the synthesis of type I collagen, resulting in bone fragility, defective dentition, ligamentous laxity, vascular fragility, and hearing impairment. In cases of severe-to-profound h...

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Autors principals: Cinzia Mariani, Filippo Carta, Emanuele Foddis, Valeria Ledda, Daniele Bernardeschi, Roberto Puxeddu
Format: Artigo
Idioma:Inglês
Publicat: Elsevier 2025-09-01
Col·lecció:Otolaryngology Case Reports
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Accés en línia:http://www.sciencedirect.com/science/article/pii/S2468548825000293
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