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Acquired angioedema due to C1 inhibitor deficiency: real-world clinical characteristics and treatment outcomes

IntroductionAcquired angioedema due to C1 inhibitor deficiency (AAE-C1INH) is a rare bradykinin-mediated condition that may mimic hereditary angioedema (HAE). Management is largely extrapolated from HAE data. Therefore, retrospective observations in AAE-C1INH are particularly valuable for informing...

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Gorde:
Xehetasun bibliografikoak
Egile Nagusiak: İlkim Deniz Toprak, Simge Erdem, Pelin Korkmaz, Derya Unal, Osman Ozan Yegit, Merve Hormet Igde, Şule Çelik Kamacı, Okan Çetin, Nida Öztop, Semra Demir, Can Tüzer, Metban Mastanzade, Tuğrul Elverdi, Mehmet Emin Sezgin, Sevgi Kalayoğlu Beşışık, Aslı Gelincik
Formatua: Artigo
Hizkuntza:Inglês
Argitaratua: Frontiers Media S.A. 2026-05-01
Saila:Frontiers in Immunology
Gaiak:
Sarrera elektronikoa:https://www.frontiersin.org/articles/10.3389/fimmu.2026.1836363/full
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