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Mast cell mediators in hereditary angioedema

Abstract Background Bradykinin-mediated hereditary angioedema due to C1 inhibitor deficiency (HAE-C1INH) is often hard to differentiate from mast cell (MC) mediated diseases. MCs can be activated by numerous stimuli, leading to the release of various mediators. Recently, crosstalk between MCs and th...

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Autors principals: Hanga Réka Horváth, Noémi Andrási, Eszter Nagy, Éva Imreh, Henriette Farkas
Format: Artigo
Idioma:Inglês
Publicat: BMC 2026-03-01
Col·lecció:Orphanet Journal of Rare Diseases
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Accés en línia:https://doi.org/10.1186/s13023-026-04294-6
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