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Pericardial Constriction and Myocardial Restriction in Pediatric Mulibrey Nanism: A Complex Disease With Diastolic Dysfunction

Background: Mulibrey nanism (MUL) is a rare condition with profound growth delay. Congestive heart failure is a major determinant of prognosis. The aim was to delineate pericardial constriction and myocardial functional abnormalities in a pediatric MUL sample. Methods: A total of 23 MUL patients and...

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Príomhchruthaitheoirí: Taisto Sarkola, MD, PhD, Marita Lipsanen-Nyman, MD, PhD, Hannu Jalanko, MD, PhD, Eero Jokinen, MD, PhD
Formáid: Artigo
Teanga:Inglês
Foilsithe / Cruthaithe: Elsevier 2022-01-01
Sraith:CJC Open
Rochtain ar líne:http://www.sciencedirect.com/science/article/pii/S2589790X21002298
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