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The Influence of Supplemental Dietary Linoleic Acid on Skeletal Muscle Contractile Function in a Rodent Model of Barth Syndrome

Barth syndrome is a rare and incurable X-linked (male-specific) genetic disease that affects the protein tafazzin (Taz). Taz is an important enzyme responsible for synthesizing biologically relevant cardiolipin (for heart and skeletal muscle, cardiolipin rich in linoleic acid), a critical phospholip...

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Autori principali: Mario Elkes, Martin Andonovski, Daislyn Vidal, Madison Farago, Ryan Modafferi, Steven M. Claypool, Paul J. LeBlanc
Natura: Artigo
Lingua:Inglês
Pubblicazione: Frontiers Media S.A. 2021-08-01
Serie:Frontiers in Physiology
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Accesso online:https://www.frontiersin.org/articles/10.3389/fphys.2021.731961/full
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