Diminished exercise capacity and mitochondrial bc1 complex deficiency in tafazzin-knockdown mice.
The phospholipid, cardiolipin, is essential for maintaining mitochondrial structure and optimal function. Cardiolipin-deficiency in humans, Barth syndrome, is characterized by exercise intolerance, dilated cardiomyopathy, neutropenia and 3-methyl-glutaconic aciduria. The causative gene is the mitoch...
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| Principais autores: | , , , |
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| Format: | Artigo |
| Sprog: | Inglês |
| Udgivet: |
Frontiers Media S.A.
2013-04-01
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| Serier: | Frontiers in Physiology |
| Fag: | |
| Online adgang: | http://journal.frontiersin.org/Journal/10.3389/fphys.2013.00074/full |
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