Delivery of the 7-dehydrocholesterol reductase gene to the central nervous system using adeno-associated virus vector in a mouse model of Smith-Lemli-Opitz Syndrome

par Pasta, Saloni, Akhile, Omoye, Tabron, Dorothy, Ting, Flora, Shackleton, Cedric, Watson, Gordon
Publié dans Mol Genet Metab Rep (2015)

Mechanism and Substrate Recognition of Human Holo ACP Synthase

par Bunkoczi, Gabor, Pasta, Saloni, Joshi, Anil, Wu, Xiaoqiu, Kavanagh, Kathryn L., Smith, Stuart, Oppermann, Udo
Publié 2007

αB-crystallin, a small heat-shock protein, prevents the amyloid fibril growth of an amyloid β-peptide and β(2)-microglobulin

par Raman, Bakthisaran, Ban, Tadato, Sakai, Miyo, Pasta, Saloni Y., Ramakrishna, Tangirala, Naiki, Hironobu, Goto, Yuji, Rao, Ch. Mohan
Publié 2005

Compromised Mitochondrial Fatty Acid Synthesis in Transgenic Mice Results in Defective Protein Lipoylation and Energy Disequilibrium

par Smith, Stuart, Witkowski, Andrzej, Moghul, Ayesha, Yoshinaga, Yuko, Nefedov, Michael, de Jong, Pieter, Feng, Dejiang, Fong, Loren, Tu, Yiping, Hu, Yan, Young, Stephen G., Pham, Thomas, Cheung, Carling, Katzman, Shana M., Brand, Martin D., Quinlan, Casey L., Fens, Marcel, Kuypers, Frans, Misquitta, Stephanie, Griffey, Stephen M., Tran, Son, Gharib, Afshin, Knudsen, Jens, Hannibal-Bach, Hans Kristian, Wang, Grace, Larkin, Sandra, Thweatt, Jennifer, Pasta, Saloni
Publié 2012