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Clinical, Immunological, and Molecular Features of Severe Combined Immune Deficiency: A Multi-Institutional Experience From India

BACKGROUND: Severe Combined Immune Deficiency (SCID) is an inherited defect in lymphocyte development and function that results in life-threatening opportunistic infections in early infancy. Data on SCID from developing countries are scarce. OBJECTIVE: To describe clinical and laboratory features of...

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Publicado en:Front Immunol
Autores principales: Vignesh, Pandiarajan, Rawat, Amit, Kumrah, Rajni, Singh, Ankita, Gummadi, Anjani, Sharma, Madhubala, Kaur, Anit, Nameirakpam, Johnson, Jindal, Ankur, Suri, Deepti, Gupta, Anju, Khadwal, Alka, Saikia, Biman, Minz, Ranjana Walker, Sharma, Kaushal, Desai, Mukesh, Taur, Prasad, Gowri, Vijaya, Pandrowala, Ambreen, Dalvi, Aparna, Jodhawat, Neha, Kambli, Priyanka, Madkaikar, Manisha Rajan, Bhattad, Sagar, Ramprakash, Stalin, CP, Raghuram, Jayaram, Ananthvikas, Sivasankaran, Meena, Munirathnam, Deenadayalan, Balaji, Sarath, Rajendran, Aruna, Aggarwal, Amita, Singh, Komal, Na, Fouzia, George, Biju, Mehta, Ankit, Lashkari, Harsha Prasada, Uppuluri, Ramya, Raj, Revathi, Bartakke, Sandip, Gupta, Kirti, Sreedharanunni, Sreejesh, Ogura, Yumi, Kato, Tamaki, Imai, Kohsuke, Chan, Koon Wing, Leung, Daniel, Ohara, Osamu, Nonoyama, Shigeaki, Hershfield, Michael, Lau, Yu-Lung, Singh, Surjit
Formato: Artigo
Lenguaje:Inglês
Publicado: Frontiers Media S.A. 2021
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC7897653/
https://ncbi.nlm.nih.gov/pubmed/33628209
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3389/fimmu.2020.619146
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