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Effects of Fe(2+)/Fe(3+) Binding to Human Frataxin and Its D122Y Variant, as Revealed by Site-Directed Spin Labeling (SDSL) EPR Complemented by Fluorescence and Circular Dichroism Spectroscopies

Frataxin is a highly conserved protein whose deficiency results in the neurodegenerative disease Friederich’s ataxia. Frataxin’s actual physiological function has been debated for a long time without reaching a general agreement; however, it is commonly accepted that the protein is involved in the b...

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Detalhes bibliográficos
Publicado no:Int J Mol Sci
Main Authors: Doni, Davide, Passerini, Leonardo, Audran, Gérard, Marque, Sylvain R. A., Schulz, Marvin, Santos, Javier, Costantini, Paola, Bortolus, Marco, Carbonera, Donatella
Formato: Artigo
Idioma:Inglês
Publicado em: MDPI 2020
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC7766144/
https://ncbi.nlm.nih.gov/pubmed/33348670
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3390/ijms21249619
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