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Novel pathogenic alterations in pediatric and adult desmoid-type fibromatosis – A systematic analysis of 204 cases

Desmoid-type fibromatosis (DTF, aggressive fibromatosis) is a non-metastasizing mesenchymal neoplasm of deep soft tissue with a tendency towards local recurrence. Genetic alterations affecting canonical Wnt/β-catenin signaling are reported in the majority of DTF. While most sporadic DTF harbor somat...

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Dettagli Bibliografici
Pubblicato in:Sci Rep
Autori principali: Trautmann, Marcel, Rehkämper, Jan, Gevensleben, Heidrun, Becker, Jessica, Wardelmann, Eva, Hartmann, Wolfgang, Grünewald, Inga, Huss, Sebastian
Natura: Artigo
Lingua:Inglês
Pubblicazione: Nature Publishing Group UK 2020
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC7042250/
https://ncbi.nlm.nih.gov/pubmed/32099073
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1038/s41598-020-60237-6
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