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The clinical and mutational spectrum of B3GAT3 linkeropathy: two case reports and literature review

BACKGROUND: Proteoglycans are large and structurally complex macromolecules which can be found in abundancy in the extracellular matrix and on the surface of all animal cells. Mutations in the genes encoding the enzymes responsible for the formation of the tetrasaccharide linker region between the p...

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Bibliografske podrobnosti
izdano v:Orphanet J Rare Dis
Main Authors: Colman, Marlies, Van Damme, Tim, Steichen-Gersdorf, Elisabeth, Laccone, Franco, Nampoothiri, Sheela, Syx, Delfien, Guillemyn, Brecht, Symoens, Sofie, Malfait, Fransiska
Format: Artigo
Jezik:Inglês
Izdano: BioMed Central 2019
Teme:
Online dostop:https://ncbi.nlm.nih.gov/pmc/articles/PMC6567438/
https://ncbi.nlm.nih.gov/pubmed/31196143
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/s13023-019-1110-9
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