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Combined deficiency of Senataxin and DNA-PKcs causes DNA damage accumulation and neurodegeneration in spinal muscular atrophy

Chronic low levels of survival motor neuron (SMN) protein cause spinal muscular atrophy (SMA). SMN is ubiquitously expressed, but the mechanisms underlying predominant neuron degeneration in SMA are poorly understood. We report that chronic low levels of SMN cause Senataxin (SETX)-deficiency, which...

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Bibliografiske detaljer
Udgivet i:Nucleic Acids Res
Main Authors: Kannan, Annapoorna, Bhatia, Kanchan, Branzei, Dana, Gangwani, Laxman
Format: Artigo
Sprog:Inglês
Udgivet: Oxford University Press 2018
Fag:
Online adgang:https://ncbi.nlm.nih.gov/pmc/articles/PMC6144794/
https://ncbi.nlm.nih.gov/pubmed/30010942
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1093/nar/gky641
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