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Lipidomic analysis of fibroblasts from Zellweger spectrum disorder patients identifies disease-specific phospholipid ratios
Peroxisomes are subcellular organelles involved in various metabolic processes, including fatty acid and phospholipid homeostasis. The Zellweger spectrum disorders (ZSDs) represent a group of diseases caused by a defect in the biogenesis of peroxisomes. Accordingly, cells from ZSD patients are expec...
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Publicado en: | J Lipid Res |
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Autores principales: | , , , , , , , |
Formato: | Artigo |
Lenguaje: | Inglês |
Publicado: |
The American Society for Biochemistry and Molecular Biology
2016
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Materias: | |
Acceso en línea: | https://ncbi.nlm.nih.gov/pmc/articles/PMC4959860/ https://ncbi.nlm.nih.gov/pubmed/27284103 https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1194/jlr.M067470 |
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