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Lipidomic analysis of fibroblasts from Zellweger spectrum disorder patients identifies disease-specific phospholipid ratios

Peroxisomes are subcellular organelles involved in various metabolic processes, including fatty acid and phospholipid homeostasis. The Zellweger spectrum disorders (ZSDs) represent a group of diseases caused by a defect in the biogenesis of peroxisomes. Accordingly, cells from ZSD patients are expec...

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Detalles Bibliográficos
Publicado en:J Lipid Res
Autores principales: Herzog, Katharina, Pras-Raves, Mia L., Vervaart, Martin A. T., Luyf, Angela C. M., van Kampen, Antoine H. C., Wanders, Ronald J. A., Waterham, Hans R., Vaz, Frédéric M.
Formato: Artigo
Lenguaje:Inglês
Publicado: The American Society for Biochemistry and Molecular Biology 2016
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC4959860/
https://ncbi.nlm.nih.gov/pubmed/27284103
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1194/jlr.M067470
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