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IgG4-related disease: a systematic review of this unrecognized disease in pediatrics

BACKGROUND: Immunoglobulin G4-related disease (IgG4-RD) is a systemic fibro-inflammatory condition with an unclear pathophysiological mechanism affecting different parts of the body. If untreated, the disease can lead to fibrosis and irreversible organ damage. IgG4-RD mostly has been described in ad...

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Библиографические подробности
Опубликовано в: :Pediatr Rheumatol Online J
Главные авторы: Karim, Faiz, Loeffen, Jan, Bramer, Wichor, Westenberg, Lauren, Verdijk, Rob, van Hagen, Martin, van Laar, Jan
Формат: Artigo
Язык:Inglês
Опубликовано: BioMed Central 2016
Предметы:
Online-ссылка:https://ncbi.nlm.nih.gov/pmc/articles/PMC4807566/
https://ncbi.nlm.nih.gov/pubmed/27012661
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/s12969-016-0079-3
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